ЭXЭМҮТ
Kasabach-Merritt syndrome is a rare type of vascular lesion with peculiar characteristics. The diagnosis is based upon three basic findings; enlarging haemangioma, thrombocytopenia and consumption coagulopathy.
A case presentation: A 1.2 month old boy was admitted to the National Center for Maternal and Child Health for management of a maxillofacial mass. He was the forth child of normal parents, born in а province following uncomplicated pregnancy and delivery. At birth a bluish birth mark was noted near the left ear. Over the next one month, this birth mark increased in size and evolved into a swelling. As a result, the patient was admitted to subprovincial and provincial hospitals and operated. Because of no any improvements after the operation the case was referred to the National Center for Maternal and Child Health for the management.The clinical findings and imagining studies followed by laboratory investigations strongly suggested the diagnosis of Kasabach-Merritt syndrome. One week after the start of corticosteroids the size of the lesion started to decrease. At the end of 5th week the lesion size decreased and the platelet count increased. Treatment with corticosteroids followed by surgical excision may be one of the best management in selected cases of Kasabach-Merritt syndrome.
